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Antibodies
Anti-FANCC Antibody
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产品名称:
Anti-FANCC Antibody
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简单介绍
Anti-FANCC
Antibody
Anti-FANCC Antibody
的详细介绍
Overview
Name:
Anti-FANCC
Antibody
See all FANCC primary antibodies
Description:
Rabbit polyclonal antibody to FANCC.
Applications:
WB, IHC, IF
Dilutions:
WB: 1:500 - 1:2000, IHC: 1:50 - 1:200, IF: 1:50 - 1:200.
Reactivity:
Human
Immunogen:
Recombinant protein of human FANCC.
Protein Length:
558
Host:
Rabbit
Clonality:
Polyclonal
Isotype:
IgG
Conjugate:
Unconjugated
Purification:
Affinity purification.
Product Form:
Liquid
Formulation:
Supplied in Phosphate Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 50% Glycerol.
Storage:
Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.
Target
Function:
DNA repair protein that may operate in a postreplication repair or a cell cycle checkpoint function. May be implicated in interstrand DNA cross-link repair and in the maintenance of normal chromosome stability. Upon IFNG induction, may facilitate STAT1 activation by recruiting STAT1 to IFNGR1.
Tissue Specificity:
Ubiquitous.
Involvement in Disease:
Fanconi anemia complementation group C: A disorder affecting all bone marrow elements and resulting in anemia, leukopenia and thrombopenia. It is associated with cardiac, renal and limb malformations, dermal pigmentary changes, and a predisposition to the development of malignancies. At the cellular level it is associated with hypersensitivity to DNA-damaging agents, chromosomal instability (increased chromosome breakage) and defective DNA repair.
Cellular Location:
Nucleus. Cytoplasm.
The major form is nuclear. The minor form is cytoplasmic.
Database Links:
Entrez Gene: 2176?Human
Omim: 613899?Human
SwissProt: Q00597?Human
Unigene: 494529?Human
Synonyms:
bA80I15.1 Antibody
FA 3 Antibody
FA3 Antibody
FAC Antibody
FACC Antibody
FANCC Antibody
FANCC_HUMAN Antibody
Fanconi anemia complementation group C Antibody
Fanconi anemia complementation group C protein Antibody
Fanconi anemia group C protein Antibody
Fanconi pancytopenia type 3 Antibody
FLJ14675 Antibody
Protein FACC Antibody
Information:
Target information shown above is from the UniProt Consortium.
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