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Antibodies
Anti-Factor IX Antibody
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产品名称:
Anti-Factor IX Antibody
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简单介绍
Anti-Factor IX
Antibody
Anti-Factor IX Antibody
的详细介绍
Overview
Name:
Anti-Factor IX
Antibody
See all Factor IX primary antibodies
Description:
Rabbit polyclonal antibody to Factor IX
Applications:
WB, IHC
Reactivity:
Human
Immunogen:
Recombinant protein fragment contain a sequence corresponding to a region within amino acids 217 and 423 of Human F9
Host:
Rabbit
Clonality:
Polyclonal
Conjugate:
Unconjugated
Purification:
Purified by antigen-affinity chromatography.
Formulation:
Supplied in 0.1M Tris-buffered saline with 20% Glycerol (pH7.0). 0.01% Thimerosal was added as a preservative.
Storage:
Store at -20?C for long term preservation (recommended). Store at 4?C for short term use.
Target
Function:
Factor IX is a vitamin K-dependent plasma protein that participates in the intrinsic pathway of blood coagulation by converting factor X to its active form in the presence of Ca(2+) ions, phospholipids, and factor VIIIa.
Tissue Specificity:
Detected in blood plasma (at protein level) (PubMed:3857619, PubMed:8295821, PubMed:2592373, PubMed:9169594, PubMed:19846852). Synthesized primarily in the liver and secreted in plasma.
Involvement in Disease:
Hemophilia B: An X-linked blood coagulation disorder characterized by a permanent tendency to hemorrhage, due to factor IX deficiency. It is phenotypically similar to hemophilia A, but patients present with fewer symptoms. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma.
Thrombophilia, X-linked, due to factor IX defect: A hemostatic disorder characterized by a tendency to thrombosis.
Sequence Similarities:
Belongs to the peptidase S1 family.
Post-Translational Modification:
Activated by factor XIa, which excises the activation peptide (PubMed:9169594, PubMed:1730085). The propeptide can also be removed by snake venom protease (PubMed:20004170, PubMed:20080729).
Cellular Location:
Secreted.
Database Links:
Entrez Gene: 2158?Human
Omim: 300746?Human
SwissProt: P00740?Human
Unigene: 522798?Human
Synonyms:
Cf-9 Antibody
Cf9 Antibody
Christmas Disease Antibody
Christmas factor Antibody
Coagulant factor IX Antibody
Coagulation factor 9 Antibody
Coagulation factor IX Antibody
Coagulation factor IXa heavy chain Antibody
F9 Antibody
F9 p22 Antibody
FA9_HUMAN Antibody
Factor 9 Antibody
Factor IX Antibody
Factor IX Deficiency Antibody
Factor IX F9 Antibody
FactorIX Antibody
FIX Antibody
FIX F9 Antibody
Haemophilia B Antibody
HEMB Antibody
MGC129641 Antibody
MGC129642 Antibody
P19 Antibody
Plasma thromboplastic component Antibody
Plasma Thromboplastin Component Antibody
PTC Antibody
THPH8 Antibody
Information:
Target information shown above is from the UniProt Consortium.
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