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Antibodies
Anti-Cytochrome c1, heme protein, mitochondrial Antibody
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产品名称:
Anti-Cytochrome c1, heme protein, mitochondrial Antibody
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简单介绍
Anti-Cytochrome c1, heme protein, mitochondrial
Antibody
Anti-Cytochrome c1, heme protein, mitochondrial Antibody
的详细介绍
Overview
Name:
Anti-Cytochrome c1, heme protein, mitochondrial
Antibody
See all Cytochrome c1, heme protein, mitochondrial primary antibodies
Description:
Rabbit polyclonal antibody to Cytochrome c1, heme protein, mitochondrial
Specificity:
The antibody detects endogenous level of total Cytochrome c1, heme protein, mitochondrial polyclonal antibody.
Applications:
WB, IHC
Reactivity:
Human
Immunogen:
Recombinant human Cytochrome c1, heme protein, mitochondrial protein
Host:
Rabbit
Clonality:
Polyclonal
Conjugate:
Unconjugated
Purification:
Caprylic Acid Ammonium Sulfate Precipitation purified
Concentration:
1.0mg / mL
Formulation:
Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
Storage:
Store at -20?C
Target
Function:
This is the heme-containing component of the cytochrome b-c1 complex, which accepts electrons from Rieske protein and transfers electrons to cytochrome c in the mitochondrial respiratory chain.
Involvement in Disease:
Mitochondrial complex III deficiency, nuclear 6: An autosomal recessive disorder caused by mitochondrial dysfunction. It is characterized by onset in early childhood of episodic acute lactic acidosis, ketoacidosis, and insulin-responsive hyperglycemia, usually associated with infection. Laboratory studies show decreased activity of mitochondrial complex III. Psychomotor development is normal.
Sequence Similarities:
Belongs to the cytochrome c family.
Post-Translational Modification:
Binds 1 heme group per subunit.
Cellular Location:
Mitochondrion inner membrane.
Database Links:
Entrez Gene: 1537?Human
Omim: 123980?Human
SwissProt: P08574?Human
Unigene: 289271?Human
Synonyms:
Complex III subunit 4 Antibody
Complex III subunit IV Antibody
CY1_HUMAN Antibody
CYC1 Antibody
Cytochrome b c1 complex subunit 4 Antibody
Cytochrome b-c1 complex subunit 4 Antibody
Cytochrome bc1 complex subunit 4 Antibody
Cytochrome c 1 Antibody
Cytochrome c-1 Antibody
Cytochrome c1, heme protein, mitochondrial Antibody
Ubiquinol cytochrome c reductase complex cytochrome c1 subunit Antibody
Ubiquinol-cytochrome-c reductase complex cytochrome c1 subunit Antibody
UQCR4 Antibody
Information:
Target information shown above is from the UniProt Consortium.
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