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Anti-CTSA Antibody

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产品名称: Anti-CTSA Antibody
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Anti-CTSA Antibody


Anti-CTSA Antibody  的详细介绍
Name: Anti-CTSA Antibody
See all CTSA primary antibodies
Description: Rabbit polyclonal antibody to CTSA.
Applications: WB, IF
Dilutions: WB: 1:500 - 1:2000, IF: 1:20 - 1:50.
Reactivity: Human, Mouse, Rat
Immunogen: Recombinant protein of human CTSA.
Protein Length: 480
Host: Rabbit
Clonality: Polyclonal
Isotype: IgG
Conjugate: Unconjugated
Purification: Affinity purification.
Product Form: Liquid
Formulation: Supplied in Phosphate Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 50% Glycerol.
Storage: Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.
Function: Protective protein appears to be essential for both the activity of beta-galactosidase and neuraminidase, it associates with these enzymes and exerts a protective function necessary for their stability and activity. This protein is also a carboxypeptidase and can deamidate tachykinins.
Involvement in Disease: Galactosialidosis: A lysosomal storage disease associated with a combined deficiency of beta-galactosidase and neuraminidase, secondary to a defect in cathepsin A. All patients have clinical manifestations typical of a lysosomal disorder, such as coarse facies, cherry red spots, vertebral changes, foam cells in the bone marrow, and vacuolated lymphocytes. Three phenotypic subtypes are recognized. The early infantile form is associated with fetal hydrops, edema, ascites, visceromegaly, skeletal dysplasia, and early death. The late infantile type is characterized by hepatosplenomegaly, growth retardation, cardiac involvement, and a normal or mildly affected mental state. The juvenile/***** form is characterized by myoclonus, ataxia, angiokeratoma, mental retardation, neurologic deterioration, absence of visceromegaly, and long survival.
Sequence Similarities: Belongs to the peptidase S10 family.
Cellular Location: Lysosome.
Database Links:
  • Entrez Gene: 5476 Human
  • Entrez Gene: 19025 Mouse
  • Entrez Gene: 296370 Rat
  • Omim: 613111 Human
  • SwissProt: P10619 Human
  • SwissProt: P16675 Mouse
  • Unigene: 609336 Human
  • Unigene: 359633 Mouse
  • Unigene: 474586 Mouse
  • Unigene: 104631 Rat
    		•
    Synonyms:
  • beta galactosidase 2 Antibody
  • BETA GALACTOSIDASE PROTECTIVE PROTEIN Antibody
  • beta-galactosidase 2 Antibody
  • beta-galactosidase protective protein Antibody
  • betagalactosidase 2 Antibody
  • Carboxypeptidase C Antibody
  • Carboxypeptidase L Antibody
  • carboxypeptidase Y-like kininase Antibody
  • Cathepsin A Antibody
  • Ctsa Antibody
  • deamidase Antibody
  • EC 3.4.16.5 Antibody
  • Glactosialidosis Antibody
  • GLB2 Antibody
  • Goldberg Syndrome Antibody
  • GSL Antibody
  • lysosomal carboxypeptidase A Antibody
  • Lysosomal protective protein Antibody
  • Lysosomal protective protein 20 kDa chain Antibody
  • Lysosomal protective protein deficiency Antibody
  • NEURAMINIDASE BETA GALACTOSIDASE EXPRESSION; NGBE Antibody
  • Neuraminidase deficiency with beta-galactosidase deficiency Antibody
  • NGBE Antibody
  • OTTHUMP00000031778 Antibody
  • OTTHUMP00000031781 Antibody
  • PPCA Antibody
  • PPCA deficiency Antibody
  • PPGB Antibody
  • PPGB_HUMAN Antibody
  • Protective protein cathepsin A Antibody
  • Protective protein for beta galactosidase Antibody
  • Protective protein for beta-galactosidase Antibody
  • Protective protein/Cathepsin A (PPCA) Antibody
  • Protective protein/cathepsin A deficiency Antibody
  • urinary kininase Antibody
    		•
    Information: Target information shown above is from the UniProt Consortium.
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