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Anti-CLN6 Antibody

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产品名称: Anti-CLN6 Antibody
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简单介绍

Anti-CLN6 Antibody


Anti-CLN6 Antibody  的详细介绍
Name: Anti-CLN6 Antibody
See all CLN6 primary antibodies
Description: Rabbit polyclonal antibody to CLN6
Specificity: The antibody detects endogenous levels of total CLN6 protein.
Applications: WB, IHC
Reactivity: Human
Immunogen: Synthesized peptide derived from internal of human CLN6.
Host: Rabbit
Clonality: Polyclonal
Conjugate: Unconjugated
Purification: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Concentration: 1.0mg / ml
Formulation: Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol.
Storage: Store at -20?C
Involvement in Disease: Ceroid lipofuscinosis, neuronal, 6: A form of neuronal ceroid lipofuscinosis. Neuronal ceroid lipofuscinoses are progressive neurodegenerative, lysosomal storage diseases characterized by intracellular accumulation of autofluorescent liposomal material, and clinically by seizures, dementia, visual loss, and/or cerebral atrophy. The lipopigment patterns observed most often in neuronal ceroid lipofuscinosis type 6 comprise mixed combinations of granular, curvilinear, and fingerprint profiles.

Ceroid lipofuscinosis, neuronal, 4A: An *****-onset neuronal ceroid lipofuscinosis. Neuronal ceroid lipofuscinoses are progressive neurodegenerative, lysosomal storage diseases characterized by intracellular accumulation of autofluorescent liposomal material, and clinically by seizures, dementia, visual loss, and/or cerebral atrophy. CLN4A has no visual involvement and is characterized by progressive myoclonic epilepsy.
Cellular Location: Endoplasmic reticulum membrane. Endoplasmic reticulum.
Database Links:
  • Entrez Gene: 54982?Human
  • Omim: 606725?Human
  • SwissProt: Q9NWW5?Human
    		•
    Synonyms:
  • Ceroid lipofuscinosis, neuronal 6, late infantile, variant Antibody
  • CLN6 Antibody
  • CLN6 protein Antibody
  • FLJ20561 Antibody
  • HsT18960 Antibody
  • Nclf Antibody
  • Protein CLN6 Antibody
    		•
    Information: Target information shown above is from the UniProt Consortium.
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