产品资料

Anti-CLN6 (N258) Antibody

如果您对该产品感兴趣的话,可以
产品名称: Anti-CLN6 (N258) Antibody
产品型号:
产品展商: 其它品牌
产品文档: 无相关文档

简单介绍

Anti-CLN6 (N258) Antibody


Anti-CLN6 (N258) Antibody  的详细介绍
Name: Anti-CLN6 (N258) Antibody
See all CLN6 primary antibodies
Description: Rabbit polyclonal antibody to CLN6 (N258)
Specificity: CLN6 (N258) pAb detects endogenous levels of CLN6 protein.
Applications: WB, IHC
Reactivity: Human, Mouse, Rat
Immunogen: Synthetic peptide, corresponding to amino acids 229-274 of Human CLN6.
Host: Rabbit
Clonality: Polyclonal
Conjugate: Unconjugated
Molecular Weight: ~ 40 kDa
Purity: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen and the purity is > 95% (by SDS-PAGE).
Product Form: 1 mg/ml in Phosphate buffered saline (PBS) with 0.05% sodium azide, approx. pH 7.2.
Involvement in Disease: Ceroid lipofuscinosis, neuronal, 6: A form of neuronal ceroid lipofuscinosis. Neuronal ceroid lipofuscinoses are progressive neurodegenerative, lysosomal storage diseases characterized by intracellular accumulation of autofluorescent liposomal material, and clinically by seizures, dementia, visual loss, and/or cerebral atrophy. The lipopigment patterns observed most often in neuronal ceroid lipofuscinosis type 6 comprise mixed combinations of granular, curvilinear, and fingerprint profiles.

Ceroid lipofuscinosis, neuronal, 4A: An *****-onset neuronal ceroid lipofuscinosis. Neuronal ceroid lipofuscinoses are progressive neurodegenerative, lysosomal storage diseases characterized by intracellular accumulation of autofluorescent liposomal material, and clinically by seizures, dementia, visual loss, and/or cerebral atrophy. CLN4A has no visual involvement and is characterized by progressive myoclonic epilepsy.
Cellular Location: Endoplasmic reticulum membrane. Endoplasmic reticulum.
Database Links:
  • Entrez Gene: 54982?Human
  • Entrez Gene: 76524?Mouse
  • Entrez Gene: 315746?Rat
  • Omim: 606725?Human
  • SwissProt: Q9NWW5?Human
  • SwissProt: A0PJN2?Mouse
    		•
    Synonyms:
  • Ceroid lipofuscinosis, neuronal 6, late infantile, variant Antibody
  • CLN6 Antibody
  • CLN6 protein Antibody
  • FLJ20561 Antibody
  • HsT18960 Antibody
  • Nclf Antibody
  • Protein CLN6 Antibody
    		•
    Information: Target information shown above is from the UniProt Consortium.
    产品留言
    标题
    联系人
    联系电话
    内容
    验证码
    点击换一张
    注：1.可以使用快捷键Alt+S或Ctrl+Enter发送信息!
    2.如有必要,请您留下您的详细联系方式!

    沪公网安备 31011202007337号