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Antibodies
Anti-ASS1 Antibody
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产品名称:
Anti-ASS1 Antibody
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简单介绍
Anti-ASS1
Antibody
Anti-ASS1 Antibody
的详细介绍
Overview
Name:
Anti-ASS1
Antibody
See all ASS1 primary antibodies
Description:
Rabbit polyclonal antibody to ASS1
Applications:
WB, IHC
Reactivity:
Human
Immunogen:
Recombinant protein fragment contain a sequence corresponding to a region within amino acids 1 and 168 of Human ASS1
Host:
Rabbit
Clonality:
Polyclonal
Conjugate:
Unconjugated
Purification:
Purified by antigen-affinity chromatography.
Formulation:
Supplied in 0.1M Tris-buffered saline with 10% Glycerol (pH7.0). 0.01% Thimerosal was added as a preservative.
Storage:
Store at -20?C for long term preservation (recommended). Store at 4?C for short term use.
Target
Function:
Is indirectly involved in the control of blood pressure.
Involvement in Disease:
Citrullinemia 1: The classic form of citrullinemia, an autosomal recessive disease characterized primarily by elevated serum and urine citrulline levels. Ammonia intoxication is another manifestation. It is a disorder of the urea cycle, usually manifesting in the first few days of life. Affected infants appear normal at birth, but as ammonia builds up in the body they present symptoms such as lethargy, poor feeding, vomiting, seizures and loss of consciousness. Less commonly, a milder form can develop later in childhood or *****hood.
Sequence Similarities:
Belongs to the argininosuccinate synthase family. Type 1 subfamily.
Database Links:
Entrez Gene: 445?Human
Omim: 603470?Human
SwissProt: P00966?Human
Unigene: 160786?Human
Synonyms:
Argininosuccinate synthase Antibody
Argininosuccinate synthase 1 Antibody
Argininosuccinate synthetase 1 Antibody
ASS Antibody
Ass-1 Antibody
ASS1 Antibody
ASSA Antibody
ASSY_HUMAN Antibody
Citrulline aspartate ligase Antibody
Citrulline--aspartate ligase Antibody
CTLN1 Antibody
Information:
Target information shown above is from the UniProt Consortium.
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