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Anti-PCK2 Antibody

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产品名称: Anti-PCK2 Antibody
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简单介绍

Anti-PCK2 Antibody


Anti-PCK2 Antibody  的详细介绍
Name: Anti-PCK2 Antibody
See all PCK2 primary antibodies
Description: Goat polyclonal antibody to PCK2.
Applications: ELISA, WB
Reactivity: Human
Immunogen: Synthetic peptide corresponding to Human PCK2 (internal region).
Sequence: KPWKPGDKEPCAH
Host: Goat
Clonality: Polyclonal
Isotype: IgG
Conjugate: Unconjugated
Purification: Purified from goat serum by ammonium sulphate precipitation followed by antigen affinity chromatography using the immunizing peptide.
Concentration: 100 µg at 0.5 mg/ml.
Product Form: Liquid
Formulation: Supplied in Tris Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 0.5% BSA.
Storage: Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.
Function: Catalyzes the conversion of oxaloacetate (OAA) to phosphoenolpyruvate (PEP), the rate-limiting step in the metabolic pathway that produces glucose from lactate and other precursors derived from the citric acid cycle.
Involvement in Disease: Mitochondrial phosphoenolpyruvate carboxykinase deficiency: Metabolic disorder resulting from impaired gluconeogenesis. It is a rare disease with less than 10 cases reported in the literature. Clinical characteristics include hypotonia, hepatomegaly, failure to thrive, lactic acidosis and hypoglycemia. Autopsy reveals fatty infiltration of both the liver and kidneys. The disorder is transmitted as an autosomal recessive trait.
Sequence Similarities: Belongs to the phosphoenolpyruvate carboxykinase [GTP] family.
Cellular Location: Mitochondrion.
Database Links:
  • Entrez Gene: 5106 Human
  • Omim: 261650 Human
  • SwissProt: Q16822 Human
  • Unigene: 75812 Human
    		•
    Synonyms:
  • EC 4.1.1.32 Antibody
  • GTP mitochondrial precursor Antibody
  • HGNC:8725 Antibody
  • mitochondrial Antibody
  • Mitochondrial phosphoenolpyruvate carboxykinase 2 Antibody
  • OTTHUMP00000164700 Antibody
  • PCK2 Antibody
  • PCKGM_HUMAN Antibody
  • PE Antibody
  • PEP carboxykinase Antibody
  • PEPCK Antibody
  • PEPCK deficiency mitochondrial Antibody
  • PEPCK M Antibody
  • PEPCK-M Antibody
  • PEPCK2 Antibody
  • Phosphoenolpyruvate carboxykinase 2 (mitochondrial) Antibody
  • Phosphoenolpyruvate carboxykinase 2 mitochondrial Antibody
  • Phosphoenolpyruvate carboxykinase [GTP] Antibody
  • Phosphoenolpyruvate carboxylase Antibody
  • Phosphopyruvate carboxylase Antibody
    		•
    Information: Target information shown above is from the UniProt Consortium.
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