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Antibodies
Anti-ACADM Antibody
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产品名称:
Anti-ACADM Antibody
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简单介绍
Anti-ACADM
Antibody
Anti-ACADM Antibody
的详细介绍
Overview
Name:
Anti-ACADM
Antibody
See all ACADM primary antibodies
Description:
Goat polyclonal antibody to ACADM.
Applications:
ELISA, WB, IHC
Reactivity:
Human
Immunogen:
Synthetic peptide corresponding to Human ACADM (C terminal).
Sequence:
C-RLIVAREHIDKYKN
Host:
Goat
Clonality:
Polyclonal
Isotype:
IgG
Conjugate:
Unconjugated
Purification:
Purified from goat serum by ammonium sulphate precipitation followed by antigen affinity chromatography using the immunizing peptide.
Concentration:
100 μg at 0.5 mg/ml.
Product Form:
Liquid
Formulation:
Supplied in Tris Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 0.5% BSA.
Storage:
Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.
Target
Function:
Acyl-CoA dehydrogenase specific for acyl chain lengths of 4 to 16 that catalyzes the initial step of fatty acid beta-oxidation. Utilizes the electron transfer flavoprotein (ETF) as an electron acceptor to transfer electrons to the main mitochondrial respiratory chain via ETF-ubiquinone oxidoreductase (ETF dehydrogenase).
Involvement in Disease:
Acyl-CoA dehydrogenase medium-chain deficiency: An inborn error of mitochondrial fatty acid beta-oxidation which causes fasting hypoglycemia, hepatic dysfunction and encephalopathy, often resulting in death in infancy.
Sequence Similarities:
Belongs to the acyl-CoA dehydrogenase family.
Post-Translational Modification:
Acetylation at Lys-307 and Lys-311 in proximity of the cofactor-s reduces catalytic activity (By similarity). These sites are deacetylated by SIRT3.
Cellular Location:
Mitochondrion matrix.
Database Links:
Entrez Gene: 34?Human
Omim: 607008?Human
SwissProt: P11310?Human
Unigene: 445040?Human
Synonyms:
ACAD 1 Antibody
ACAD1 Antibody
ACADM Antibody
ACADM_HUMAN Antibody
Acyl coenzyme A dehydrogenase Antibody
Acyl coenzyme A dehydrogenase C 4 to C 12 straight chain Antibody
FLJ18227 Antibody
FLJ93013 Antibody
FLJ99884 Antibody
MCAD Antibody
MCADH Antibody
Medium chain acyl CoA dehydrogenase Antibody
Medium chain fatty acyl CoA dehydrogenase Antibody
Medium chain specific acyl CoA dehydrogenase Antibody
Medium chain specific acyl CoA dehydrogenase mitochondrial Antibody
Medium-chain specific acyl-CoA dehydrogenase Antibody
mitochondrial Antibody
Information:
Target information shown above is from the UniProt Consortium.
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